Kartagener Syndrome With Focal Segmental Glomerulosclerosis

Momeni, Ali and Doroushi, Behzad and Taheri, Nadia (2013) Kartagener Syndrome With Focal Segmental Glomerulosclerosis. IRANIAN JOURNAL OF KIDNEY DISEASES, 7 (6). pp. 499-501.

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Abstract

Primary ciliary dyskinesia is characterized by congenital impairment of mucociliary clearance. Kartagener syndrome (KS) is a clinical variant of primary ciliary dyskinesia which is involved in situs inversus associated with chronic respiratory infections. In addition, glomerular disease in KS syndrome is rare and reported cases are limited. We had a 27-year-old female patient with KS who presented with proteinuria, hematuria, normal kidney function, and a family history of systemic lupus erythematosus. Kidney biopsy showed segmental scar with adhesion to Bowman capsule, which was indicative of focal segmental glomerulosclerosis.

Item Type: Article
Uncontrolled Keywords: Kartagener syndrome; focal segmental glomerulosclerosis; hematuria
Subjects: WF Respiratory System
WJ Urogenital System
Divisions: Faculty of Medicine > Department of Clinical Sciences > Department of Orthopedics
Faculty of Medicine > Department of Clinical Sciences > Department of Pathology
Faculty of Medicine > Department of Clinical Sciences > Department of Urology
Depositing User: Users 1 not found.
Date Deposited: 07 Aug 2017 08:19
Last Modified: 07 Aug 2017 08:19
URI: http://eprints.skums.ac.ir/id/eprint/2522

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